Extensive cervical-mediastinal cystic lymphatic malformation treated with sclerotherapy in a child with Klippet-Trenaunay syndrome


Duman L. , KARNAK İ., AKINCI D., TANYEL F. C.

JOURNAL OF PEDIATRIC SURGERY, vol.41, no.1, 2006 (Journal Indexed in SCI) identifier identifier identifier

  • Publication Type: Article / Article
  • Volume: 41 Issue: 1
  • Publication Date: 2006
  • Doi Number: 10.1016/j.jpedsurg.2005.10.067
  • Title of Journal : JOURNAL OF PEDIATRIC SURGERY
  • Keywords: Klippet-Trenaunay syndrome, cystic lymphatic malformation, mediastinum, sclerotherapy

Abstract

Klippel-Trenaunay syndrome is a rare congenital disorder characterized by combined vascular malformations, varicosities, and limb enlargement. A child case of Klippel-Trenaunay syndrome with a large cervicomediastinal cystic lymphatic malformation and a vascular mass on the chest wall has been presented to demonstrate combined use of conservative and surgical approaches in this syndrome. Cystic lymphatic malformation was treated by sclerotherapies including ultrasound-guided transthoracic bleomycin injection into mediastinal cyst, which was tried for the first time in the literature, and vascular chest wall tumor necessitated surgical excision. (c) 2006 Elsevier Inc. All rights reserved.