Huge inflammatory myofibroblastic tumor of pleura with concomitant nuchal fibroma


Döngel İ. , Yazkan R. , Duman L. , Öztürk Ö. , Kapucuoglu F. N.

Annals of Thoracic Surgery, vol.96, pp.1461-1464, 2013 (Journal Indexed in SCI) identifier identifier identifier

  • Publication Type: Article / Article
  • Volume: 96
  • Publication Date: 2013
  • Doi Number: 10.1016/j.athoracsur.2013.01.082
  • Title of Journal : Annals of Thoracic Surgery
  • Page Numbers: pp.1461-1464

Abstract

Inflammatory myofibroblastic tumor (IMT) is a rare benign neoplasm. It is a challenging disease because the symptoms and radiologic findings are diverse and nonspecific. Although pulmonary IMT is the most common form, pleural origin is an extremely rare clinical entity. Nuchal fibroma (NF) is another rare benign neoplasm. We report herein a case of pleural IMT with concomitant NF in a 15-year-old girl. To the best of our knowledge, this is the first report suggesting an association between IMT and NF, and our case had the largest reported intrathoracic IMT. Moreover, we found a possible association between IMT and increased CA-125 levels.