Pulmonary artery dissection is a rare condition that often occurs on the basis of pulmonary arterial hypertension and causes complications such as cardiogenic shock and sudden death. Additionally, this condition can be idiopathic. A 59-year-old male patient with no previous history of disease presented to our clinic with chest pain and shortness of breath. Coronary arteries were normal on coronary angiography in the patient who had a positive troponin test result and ST segment elevation in leads V1, V2, V3 and aVR. Pulmonary embolism was suspected in the patient whose condition worsened. Pulmonary artery dissection was diagnosed via the contrast-enhanced computed tomography and sudden cardiac death occurred. In conclusion, pulmonary artery dissection may cause aVR segment elevation on electrocardiography.