Ectopic ureter in adult female patients usually presents with urinary incontinence. Clinical manifestations include incontinence and urinary tract infections. Here we report a case of ectopic megaureter opening to urethra which caused incontinence and obstructive urinary symptoms in a 19 years old woman. When we reviewed the literature, we found several cases regarding ectopic ureter associated with a single (nonduplicated) collecting system opening to the urethra. Typically, the diagnosis is made after a long delay. Surgical reconstruction of an ectopic ureter should be planned according to the degree of renal function. Most patients are cured with ureteroneocystostomy or nephroureterectomy. However, following these surgical procedures, some incontinent women may have persistent urinary incontinence due to mal-development of the bladder neck and sphincter or Gartner's duct cyst.