A case of Amyopathic Dermatomyositis associated with Interstitial Pulmonary Disease


Ugan Y., Sahin M., Dogru A., Bayram D., Ceyhan A. M. , Tunc S. E.

CLINICA TERAPEUTICA, vol.166, no.6, pp.253-255, 2015 (Journal Indexed in ESCI) identifier identifier identifier

  • Publication Type: Article / Article
  • Volume: 166 Issue: 6
  • Publication Date: 2015
  • Doi Number: 10.7417/ct.2015.1897
  • Title of Journal : CLINICA TERAPEUTICA
  • Page Numbers: pp.253-255

Abstract

Inflammatory myopathies are a heterogeneous group of diseases with unknown etiology characterized by inflammation of the skeletal muscles and proximal muscle weakness. Dermatomyositis (DM) is an idiopathic inflammatory myopathy with characteristic cutaneous findings such as heliotrope rash, Gottron's sign, Gottron's papules, shawl sign and machinist hand. Amyopathic dermatomyositis (ADM) is a rare but well-recognized clinical subtype of DM, constituting aproximately 10-20% of patients with this disease. It generally manifests only pathognomonic skin findings without clinical and laboratory evidence of muscle involvement. In this report, we present a rare case of ADM associated with interstitial pulmonary disease.